Caring for Patients With Cystic Fibrosis
About half of the individuals with cystic fibrosis (CF) in the United States are children and adolescents younger than 18. Historically, dental caries may not have been a high priority health problem among those with CF because of shortened life expectancy. Recent improvements in the management of CF and the subsequent increase in life expectancy, however, mean that dental caries prevention should be considered an integral part of comprehensive infection prevention plans. In order to help individuals with CF prevent dental caries, oral health professionals need to understand the specific risk factors that affect pediatric patients with CF and how to manage caries risk in children and adolescents with CF.
Cystic fibrosis (CF) is the least common lethal genetic disease in Caucasians.

Approximately how many individuals are diagnosed with CF in the US each year?

CF is caused by an autosomal recessive mutation to the cystic fibrosis transmembrane regulator (CFTR) gene.

Today, what percentage of individuals with CF are diagnosed by newborn screening panels that are mandated in all 50 states?

Enamel defects—often present on the maxillary incisors—were among the earliest reported dental anomalies described in individuals with CF.

Gastroesophageal reflux diseasecan also force stomach acid into the oral cavity, which, depending on frequency and severity of the acid reflux, can erode the teeth.

Preventive care for individuals with CF should center on which of the following?

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